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ICD-10-CM I27.841: Fontan-associated lymphatic dysfunction

I27.841 is the billable ICD-10-CM code for fontan-associated lymphatic dysfunction, in category I27 (Other pulmonary heart diseases) of the Pulmonary heart disease and diseases of pulmonary circulation section. As a principal diagnosis it groups to MS-DRG 808 Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders with MCC, MS-DRG 809 Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders with CC, MS-DRG 810 Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders without CC/MCC (MDC 16 MDC 16: Diseases and Disorders of Blood, Blood Forming Organs and Immunologic Disorders). 14 LCD billing and coding articles list it as covered.

Compiled from CMS files by the QuickIntell RCM Editorial Team · Data effective · Method: reference methodology · Report a data correction

Data currency: ICD-10-CM code descriptions: FY2027 (effective October 1, 2026); IPPS Table 5 (MS-DRG weights): v44 FY2027 (final rule + CN3) (effective October 1, 2026); ICD-10-CM to HCC mapping: PY2027 initial ICD-10-CM mappings (dates of service 2026) (payment year 2027); Medicare Coverage Database billing and coding articles: MCD release October 8, 2026 (effective October 4, 2026). Next CMS release: FY2028 code files, effective October 1, 2027 for the ICD-10-CM code descriptions; FY2028 final rule (August 2027), effective October 1, 2027; an April 1 interim grouper update when CMS issues one for the IPPS Table 5 (MS-DRG weights); PY2028 advance notice (February 2027) and the PY2027 midyear final mapping (spring 2027) for the ICD-10-CM to HCC mapping; weekly, every Thursday for the Medicare Coverage Database billing and coding articles.

Code
I27.841
billable FY2027 ICD-10-CM code
Category
I27 Other pulmonary heart diseases
Chapter
9: Diseases of the circulatory system (I00-I99)
CC/MCC (MS-DRG v44)
Neither
CMS-HCC V28
Not mapped
POA reporting
Required

Tabular list notes for I27.841

The tabular list has no notes on I27.841 itself; the notes below apply from its parent headings.

MS-DRG grouping when I27.841 is the principal diagnosis

MS-DRG v44 groups for I27.841 as principal diagnosis
MDCMS-DRGs
16 MDC 16: Diseases and Disorders of Blood, Blood Forming Organs and Immunologic Disorders808809810

The final group also depends on procedures, secondary diagnoses and discharge status; the MS-DRG lookup for I27.841 shows the full grouping logic.

CC/MCC status and inpatient edits

I27.841 is neither a CC nor an MCC under MS-DRG v44, so as a secondary diagnosis it does not raise the MS-DRG severity level. Check I27.841 against a principal diagnosis.

  • Present on admission: a POA indicator is required on inpatient claims.

CMS-HCC V28 risk adjustment

I27.841 does not map to a payment HCC in the PY2027 CMS-HCC V28 model, so on its own it does not change a Medicare Advantage risk score.

LCD billing and coding articles that list I27.841

14 current Medicare billing and coding articles list I27.841 among the diagnoses that support medical necessity for the services they cover.

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Frequently asked questions

What does ICD-10-CM I27.841 mean?

I27.841 means fontan-associated lymphatic dysfunction. It is one of 17 billable codes under I27, other pulmonary heart diseases.

Which MS-DRG does I27.841 group to?

As the principal diagnosis, I27.841 groups to MS-DRG 808 Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders with MCC, MS-DRG 809 Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders with CC, MS-DRG 810 Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders without CC/MCC (MDC 16 MDC 16: Diseases and Disorders of Blood, Blood Forming Organs and Immunologic Disorders) under MS-DRG v44, before procedures and secondary diagnoses are applied.

Sources

Every figure on this page is taken from the CMS publications below, as released by the Centers for Medicare & Medicaid Services. Projection built 2026-10-10. Verify against the primary file before billing or contracting decisions. The reference methodology explains how each figure is computed from these files.

Disclaimer

The descriptor and notes are reproduced from the FY2027 ICD-10-CM files; MS-DRG, CC/MCC and HCC facts come from the CMS FY2027 and PY2027 tables. Code from the medical record and the ICD-10-CM Official Guidelines. Not legal, clinical or billing advice.

Found a figure that does not match the CMS file? Report a data correction with the CMS file and the value you expected; the request reaches the editorial team through the contact form.