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ICD-10-CM category I01: Rheumatic fever with heart involvement

Category I01 is a heading in chapter 9 (Diseases of the circulatory system (I00-I99)), section Acute rheumatic fever (I00-I02). It is not billable; report one of the 5 complete codes below.

Notes that apply to every I01 code

Excludes1 (never coded together)
  • chronic diseases of rheumatic origin (I05-I09) unless rheumatic fever is also present or there is evidence of reactivation or activity of the rheumatic process.

Billable codes in I01

Billable FY2027 ICD-10-CM codes in category I01
CodeDescription
I01.0Acute rheumatic pericarditis
I01.1Acute rheumatic endocarditis
I01.2Acute rheumatic myocarditis
I01.8Other acute rheumatic heart disease
I01.9Acute rheumatic heart disease, unspecified

Sources

Every figure on this page is taken from the CMS publications below, as released by the Centers for Medicare & Medicaid Services. Projection built 2026-10-10. Verify against the primary file before billing or contracting decisions. The reference methodology explains how each figure is computed from these files.

Codes from the FY2027 ICD-10-CM files (all chapters). Report the code that matches the documentation and the Official Guidelines; this list is not coding advice.